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De første symptomene på Churg-Strauss syndrom er ofte uspesifikke, for eksempel langvarig hoste, snue og bihulebetennelse.
De første symptomene på Churg-Strauss syndrom er ofte uspesifikke, for eksempel langvarig hoste, snue og bihulebetennelse.

Eosinofil granulomatose med polyangiitt (Churg-Strauss syndrom)

Eosinofil granulomatose med polyangiitt, tidligere kalt Churg-Strauss syndrom, er en sjelden sykdom som nesten utelukkende oppstår hos personer med astma. Årsaken er ukjent.

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Den ligger åpent tilgjengelig på NHI.no sammen annen relevant informasjon

https://nhi.no/sykdommer/hud/diverse/churg-strauss-syndrom/ 

Hva er eosinofil granulomatose med polyangiitt (EGPA)?

Årsak

Symptomer

Diagnosen

Behandling

Prognose

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Referanser

Dette dokumentet er basert på det profesjonelle dokumentet Eosinofil granulomatose med polyangiitt (Churg-Strauss). Referanselisten for dette dokumentet vises nedenfor.

  1. King TE. Clinical features and diagnosis of eosinophilic granulomatosis with polyangiitis (Churg-Strauss). UpToDate, last updated Feb 15, 2018. UpToDate 
  2. Groh M, Pagnoux C, Baldini C, et al. Eosinophilic granulomatosis with polyangiitis (Churg-Strauss) (EGPA) Consensus Task Force recommendations for evaluation and management. Eur J Intern Med. 2015;26:545-553. PubMed 
  3. Sinico RA, Bottero P. Churg-Strauss angiitis. Best Pract Res Clin Rheumatol 2009; 23:355. PubMed 
  4. Ntatsaki E, Carruthers D, Chakravarty K, et al; BSR and BHPR Standards, Guidelines and Audit Working Group. BSR and BHPR guideline for the management of adults with ANCA-associated vasculitis. Rheumatology (Oxford). 2014;53:2306-2309. PubMed 
  5. Bibby S, Healy B, Steele R, et al. Association between leukotriene receptor antagonist therapy and Churg-Strauss syndrome: an analysis of the FDA AERS database. Thorax 2010; 65:132. PubMed 
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  7. Comarmond C, Pagnoux C, Khellaf M, et al. Eosinophilic granulomatosis with polyangiitis (Churg-Strauss): clinical characteristics and long-term followup of the 383 patients enrolled in the French Vasculitis Study Group cohort. Arthritis Rheum 2013; 65:270. PubMed 
  8. Churg J, Strauss L. Allergic granulomatosis, allergic angiitis, and periarteritis nodosa. Am J Pathol 1951; 27: 277-301. PubMed 
  9. Masi AT, Hunder GG, Lie JT, et al. The American College of Rheumatology 1990 criteria for the classification of Churg-Strauss syndrome (allergic granulomatosis and angiitis). Arthritis Rheum 1990; 33: 1094-100. PubMed 
  10. Cottin V, Bel E, Bottero P, et al. Revisiting the systemic vasculitis in eosinophilic granulomatosis with polyangiitis (Churg-Strauss): A study of 157 patients by the Groupe d'Etudes et de Recherche sur les Maladies Orphelines Pulmonaires and the European Respiratory Society Taskforce on eosinophilic granulomatosis with polyangiitis (Churg-Strauss). Autoimmun Rev 2017; 16:1. PubMed 
  11. King TE. Treatment and prognosis of eosinophilic granulomatosis with polyangiitis (Churg-Strauss). UpToDate, last updated Jun 23, 2020. UpToDate 
  12. Bel EH, Wenzel SE, Thompson PJ, et al. Oral Glucocorticoid-Sparing Effect of Mepolizumab in Eosinophilic Asthma. N Engl J Med 2014; 371: 1189-97. doi:10.1056/NEJMoa1403291 DOI 
  13. Ortega HG, Liu MC, Pavord ID, et al. Mepolizumab Treatment in Patients with Severe Eosinophilic Asthma. N Engl J Med 2014; 371: 1198-1207. doi:10.1056/NEJMoa1403290 DOI