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Budd-Chiaris syndrom

Sist revidert:
Sist revidert av:


Definisjon:
Budd-Chiaris syndrom oppstår som følge av obstruksjon av leverens venøse avløp, vanligvis som følge av trombose
Forekomst:
Meget sjelden tilstand der insidensen er beregnet til å være 1 tilfelle per 2,5 millioner per år
Symptomer:
Kan være øm og smertefull hepatomegali, ev. rask ascitesutvikling, ev. ikterus
Funn:
Ømhet under h. kostalbue, ev. hepatosplenomegali, ev. ascites, ev. ikterus, ev. akutt sykdomsbilde
Diagnostikk:
Blodprøver viser endringer i leverfunksjon og koagulasjonsfaktorer. Ultralyd, CT, MR kan demonstrere patologien
Behandling:
Har som mål å reetablere sirkulasjonen gjennom leveren
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  8. Lai M. Budd-Chiari syndrome: Management. UpToDate, last updated Nov 15, 2018. www.uptodate.com  
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  • Terje Johannessen, professor i allmennmedisin, Trondheim (tilpasning til NEL)