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Selv om Wilms svulst er sjelden, utgjør den cirka 6 prosent av alle kreftsykdommer i barneårene.
Selv om Wilms svulst er sjelden, utgjør den cirka 6 prosent av alle kreftsykdommer i barneårene.

Wilms tumor

Wilms tumor (svulst), også kalt nefroblastom, er en kreftsvulst i nyren hos barn. Prognosen etter behandling er god.

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Den ligger åpent tilgjengelig på NHI.no sammen annen relevant informasjon

https://nhi.no/sykdommer/barn/kreftsykdommer/wilms-svulst/ 

Hva er Wilms svulst?

Årsak

Symptomer

Diagnosen

Behandling

Prognose

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Referanser

Dette dokumentet er basert på det profesjonelle dokumentet Wilms tumor. Referanselisten for dette dokumentet vises nedenfor.

  1. Batra S. Wilms' tumour. BMJ Best Practice, last reviewed 3 Aug 2021. bestpractice.bmj.com 
  2. Kaste SC, Dome JS, Babyn PS, et al. Wilms tumour: prognostic factors, staging, therapy and late effects. Pediatr Radiol. 2008 Jan;38(1):2-17. PubMed 
  3. Chintagumpala M, Muscal JA. Presentation, diagnosis, and staging of Wilms tumor. UpToDate, last updated April 24, 2015 . UpToDate 
  4. Ruteshouser EC, Robinson SM, Huff V. Wilms tumor genetics: mutations in WT1, WTX, and CTNNB1 account for only about one-third of tumors. Genes Chromosomes Cancer. 2008 June;47(6):461-70. PubMed 
  5. Servaes S, Khanna G, Naranjo A, et al. Comparison of diagnostic performance of CT and MRI for abdominal staging of pediatric renal tumors: a report from the Children's Oncology Group. Pediatr Radiol 2015; 45:166. PubMed 
  6. Smets AM, van Tinteren H, Bergeron C, et al. The contribution of chest CT-scan at diagnosis in children with unilateral Wilms' tumour. Results of the SIOP 2001 study. Eur J Cancer 2012; 48:1060. PubMed 
  7. Dome JS, Graf N, Geller JI, et al. Advances in Wilms Tumor Treatment and Biology: Progress Through International Collaboration. J Clin Oncol 2015; 33: 2999-3007. pmid:26304882 PubMed 
  8. Fernandez CV, Perlman EJ, Mullen EA, et al. Clinical Outcome and Biological Predictors of Relapse After Nephrectomy Only for Very Low-risk Wilms Tumor: A Report From Children's Oncology Group AREN0532. Ann Surg 2017; 265: 835. pmid:27811504 PubMed 
  9. D'Angio GJ. The National Wilms Tumor Study: a 40 year perspective. Lifetime Data Anal. 2007 Dec;13(4):463-70. PubMed