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Periodisk feber-syndrom hos barn

Sist revidert:
Sist revidert av:
Definisjon:
Regelmessig tilbakevendende episoder med feber med 4-6 ukers intervall. Etiologi og patogenese er ukjent.
Forekomst:
I et lite norsk materiale fant man en insidens på 2,3 per 10 000 barn under 5 år per år
Symptomer:
Regelmessig forekomst av høy feber ledsaget av faryngitt eller tonsilitt, cervikal lymfadenitt og hos de fleste after
Funn:
Typiske kliniske funn er cervikal lymfadenitt, tonsillitt/faryngitt, aftøs stomatitt
Diagnostikk:
Utredning for å utelukke infeksjon og andre periodiske febersyndromer er aktuelt
Behandling:
Tilstanden går over uten behandling. Antibiotika har ingen effekt. Steroider eller tonsillektomi er noen ganger aktuelt
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  15. Burton MJ, Pollard AJ, Ramsden JD et al. Tonsillectomy for periodic fever, aphthous stomatitis, pharyngitis and cervical adenitis syndrome (PFAPA). Cochrane Database of Systematic Reviews 2019, Issue 12. Art. No.: CD008669. DOI: 10.1002/14651858.CD008669.pub3. DOI  
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  • Silje Folven Barlindhaug, spesialist allmennmedisin, redaktør NEL

Tidligere fagmedarbeidere

  • Kurt Østhuus Krogh, spesialist i barnesykdommer, Barne- og ungdomsklinikken, St. Olavs Hospital, Trondheim